Sturge weber syndrome is usually manifested at birth by a port wine stain on the forehead and upper eyelid of one side of the face or the whole face. Sturge weber syndrome b.
When found in the lungs tram tracks are radiologic signs that are usually accompanied by pulmonary edema in cases of congestive heart failure and bronchiectasis.
Tram track appearance in sturge weber syndrome. Question tram track appearance on ct scan of head is seen in the diagram a. Open in read by qxmd. Physical and family history variables associated with neurological and cognitive development in sturge weber syndrome.
Review of literature with case illustration romanian neurosurgery vol. Tram tracks are caused by bronchial wall thickening and can be detected on a lateral chest x ray. Sturge weber syndrome or encephalotrigeminal angiomatosis is a phakomatosis characterized by facial port wine stains and pial angiomas.
Am j med genet. On mr imaging t1 weighted imaging with contrast shows leptomeningeal enhancement this may not be seen in older patients. Sturge weber syndrome sws is a neurological disorder marked by a distinctive port wine stain on the forehead scalp or around the eye.
It is part of a wide spectrum of possible phenotypes included in the craniofacial arteriovenous metameric syndrome cams. This stain is a birthmark caused by an overabundance of. Day am mcculloch ce hammill am et al.
It is best seen by silver and pas stains. The hallmark of sws is a facial cutaneous veno. The birthmark can vary in color from light pink to deep purple and is caused by an overabundance of capillaries around the ophthalmic branch of the trigeminal nerve just under the surface of the face.
On ct imaging gyral subcortical calcification is seen with a tram track appearance unilateral cerebral atrophy can also be appreciated. Sujansky e conradi s. Neurofibroma show answer correct answer a explanation tram track appearance on ct scan of head is seen in struge weber syndrome.
Pathology tram track appearance refers to parallel thickening and splitting of the glomerular capillary basement membrane due to subendothelial deposition of immune complexes mesangial matrix and neutrophilic debris between the glomerular basement membrane and the vascular endothelium causing a double contour by light microscopy a classic finding in type i less in type ii membranoproliferative glomerulonephritis and cryoglobulinemia. Von hipple lindau syndrome c. Sturge weber syndrome sws also called encephalotrigeminal angiomatosis is a neurocutaneous disorder with angiomas that involve the leptomeninges leptomeningeal angiomas las and the skin of the face typically in the ophthalmic v1 and maxillary v2 distributions of the trigeminal nerve.
Imaging characteristics of sturge weber syndrome. Outcome of sturge weber syndrome in 52 adults. 1 a case of 55 year old man with first ever generalized seizure diagnosed with sturge weber syndrome type iii by characteristic mri findings.